Pleural Sarcoma, Epos Trade

4x and 20x he images of pleural synovial sarcoma.

North lawrence ohio. Primary pleural synovial sarcoma is extremely uncommon and its therapeutic strategy has not been clearly established 1. Here we report the case of a patient with primary pleural synovial sarcoma who had repeated surgery for ipsilateral pleural recurrent lesions and remains alive 12 years after the initial surgery. It together with primary synovial sarcoma of the lung comes under the broader category of pleuro pulmonary synovial sarcomas.

Synovial sarcoma is a soft tissue malignant tumour and the majority of that occur in extremities. There are several tumors that can involve the pleura which can range from being benign to malignant. There is a large mass in the right upper hemithorax peripherally.

The chest x ray showed a left basal opacity of lobulated contours and the thoracic computer tomography ct scan revealed a left pleural collectionmass of 18 hu density and passive pulmonary atelectasis. Primary pleural sarcomas are very rare. A histologically on the scanning power the lesion shows alveolar ling tissue with the sarcoma.

A pleural tumor is almost always metastatic cancerous and difficult to operate on. 1 3 however most of the histological types have been described in this location including synovial sarcoma malignant fibrous histocytoma primitive neuroectodermal tumourewing sarcoma angiosarcoma chondrosarcoma osteosarcoma and liposarcomas. Identification of these tumors is clinically relevant due to their aggressive behavior poor prognosis and potential targeted therapy.

The diagnosis is made after excluding metastasis from an extrathoracic sarcoma. Pleural tumors are found in the pleural spacethe cavity between the lungs and chest wall that contains lubricating pleural fluid. Primary pleural liposarcoma ppl is a rare tumor derived from primitive mesenchymal tissue.

B on higher power the lesion show highly cellular spindle cells areas that are densely packed into an interwoven herringbone pattern. This is closely related to the superior aspect of the right oblique fissure and is felt most likely pleural in origin. Smarca4 deficient thoracic sarcomas can be identified based on their distinctive high grade rhabdoid morphology and the diagnosis can be confirmed by immunohistochemistry.

We report a case of a 67yearold gentleman who presented with an incidental finding of a left lung mass on a routine chest xray. Primary pleural synovial sarcoma ppss is an extremely rare malignancy without a known cause. The prognosis is seldom encouraging.

Pleural synovial sarcoma is a rare tumor and refers to a primary synovial sarcoma arising from the pleura. Tumour diagnosis is mainly based on pathologic examination and immunohistochemistry.